15 years journey of idiopathic pulmonary arterial hypertension with BMPR2 mutation
Abstract Pulmonary arterial hypertension (PAH) is known as one of diseases with the worst prognosis.Recently, targeted PAH drugs have been developed and approved for use; therefore, the treatment strategy sein?lle taitettava ty?p?yt? and goals have changed, and the prognosis has improved over two decades.We reviewed the case of a female who showed